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Posterior cortical atrophy (PCA), also cal … Posterior cortical atrophy (PCA), also called Benson's syndrome, is a rare form of dementia which is considered a visual variant or an atypical variant of Alzheimer's disease (AD). The disease causes atrophy of the posterior part of the cerebral cortex, resulting in the progressive disruption of complex visual processing. PCA was first described by D. Frank Benson in 1988. PCA usually affects people at an earlier age than typical cases of Alzheimer's disease, with initial symptoms often experienced in people in their mid-fifties or early sixties. This was the case with writer Terry Pratchett (1948–2015), who went public in 2007 about being diagnosed with PCA. In rare cases, PCA can be caused by dementia with Lewy bodies and Creutzfeldt–Jakob disease.Lewy bodies and Creutzfeldt–Jakob disease.
, Posterieure corticale atrofie, syndroom va … Posterieure corticale atrofie, syndroom van Benson of ziekte van Benson is een uiterst zeldzame vorm van dementie, afgekort als PCA. De ziekte is door Benson in 1988 voor het eerst beschreven. Deze progressieve hersenaandoening start met het atrofiëren van de kleine hersenen of de cortex parietalis posterior. De eerste symptomen zijn veelal in verminderde waarneming, onhandigheid en afnemende ruimtelijke oriëntatie. Door de moeizame informatieverwerking neemt de geestelijke belastbaarheid eveneens af. De ziekte mondt uit in de ziekte van Alzheimer doordat de aantasting ook de prefrontale cortex bereikt. De levensverwachting is vanaf het punt dat de eerste symptomen zich voordoen, veelal 8-10 jaar en soms langer.voordoen, veelal 8-10 jaar en soms langer.
, L'atrophie corticale postérieure (ACP), ég … L'atrophie corticale postérieure (ACP), également appelée syndrome de Benson, est une maladie neurodégénérative rare et évolutive, apparaissant essentiellement entre 50 et 65 ans. C'est une forme de démence parfois considérée comme une variante atypique précoce de la maladie d'Alzheimer. Les causes ou facteurs de risques de cette maladie sont inconnus. Le docteur Frank Benson a décrit pour la première fois ce syndrome en 1988.pour la première fois ce syndrome en 1988.
, ضمور القشرية الخلفية (بالإنجليزية: Posteri … ضمور القشرية الخلفية (بالإنجليزية: Posterior cortical atrophy) أو متلازمة بنسون هو أحد أشكال الخرف، والذي يعتبر نوعا شاذا من مرض آلزهايمر. يتسبب المرض في ضمور الجزء الخلفي من القشرة المخية، وينتج عنه ضعف الرؤية تدريجيًا. اكتشف المرض لأول مرة في سنة 1988 على يد الدكتور فرانك بنسون.رة في سنة 1988 على يد الدكتور فرانك بنسون.
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rdfs:comment |
L'atrophie corticale postérieure (ACP), ég … L'atrophie corticale postérieure (ACP), également appelée syndrome de Benson, est une maladie neurodégénérative rare et évolutive, apparaissant essentiellement entre 50 et 65 ans. C'est une forme de démence parfois considérée comme une variante atypique précoce de la maladie d'Alzheimer. Les causes ou facteurs de risques de cette maladie sont inconnus. Le docteur Frank Benson a décrit pour la première fois ce syndrome en 1988.pour la première fois ce syndrome en 1988.
, ضمور القشرية الخلفية (بالإنجليزية: Posteri … ضمور القشرية الخلفية (بالإنجليزية: Posterior cortical atrophy) أو متلازمة بنسون هو أحد أشكال الخرف، والذي يعتبر نوعا شاذا من مرض آلزهايمر. يتسبب المرض في ضمور الجزء الخلفي من القشرة المخية، وينتج عنه ضعف الرؤية تدريجيًا. اكتشف المرض لأول مرة في سنة 1988 على يد الدكتور فرانك بنسون.رة في سنة 1988 على يد الدكتور فرانك بنسون.
, Posterior cortical atrophy (PCA), also cal … Posterior cortical atrophy (PCA), also called Benson's syndrome, is a rare form of dementia which is considered a visual variant or an atypical variant of Alzheimer's disease (AD). The disease causes atrophy of the posterior part of the cerebral cortex, resulting in the progressive disruption of complex visual processing. PCA was first described by D. Frank Benson in 1988.irst described by D. Frank Benson in 1988.
, Posterieure corticale atrofie, syndroom va … Posterieure corticale atrofie, syndroom van Benson of ziekte van Benson is een uiterst zeldzame vorm van dementie, afgekort als PCA. De ziekte is door Benson in 1988 voor het eerst beschreven. Deze progressieve hersenaandoening start met het atrofiëren van de kleine hersenen of de cortex parietalis posterior. De eerste symptomen zijn veelal in verminderde waarneming, onhandigheid en afnemende ruimtelijke oriëntatie. Door de moeizame informatieverwerking neemt de geestelijke belastbaarheid eveneens af. De ziekte mondt uit in de ziekte van Alzheimer doordat de aantasting ook de prefrontale cortex bereikt. De levensverwachting is vanaf het punt dat de eerste symptomen zich voordoen, veelal 8-10 jaar en soms langer.voordoen, veelal 8-10 jaar en soms langer.
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rdfs:label |
ضمور القشرية الخلفية
, Posterieure corticale atrofie
, Atrophie corticale postérieure
, Posterior cortical atrophy
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